Pentalogy of Cantrell
Pentalogy of Cantrell
Pentalogy of Cantrell
Five defects of the pentalogy as described in Cantrell’s initial paper are as follows:
- Supraumbilical omphalocele
- Lower sternal cleft
- Defect in the central tendon of the diaphragm
- Defect in the pericardium
- Intracardiac anomaly
Pericardial Defects
- Pericardial effusion is found in some cases, although relatively less severe and defects in pericardium do not present an immediate threat to life.
- It can present with muffled heart sound on cardiac auscultation.
Cardiac Defects may be present
- Atrial septal defects
- Ventricle septal defects
- Left ventricular diverticulum
- Dextrocardia
- Pulmonary stenosis
- Tetralogy of Fallot have all been associated with this disease